In which Mantle Edge Syndrome it is a damage to the jacket edge. This is accompanied by brain damage. This primarily causes a movement and sensitivity disorder of the legs.
What is coat edge syndrome?
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The Mantle Edge Syndrome is a very rare disease. The longitudinal fissure of the cerebrum is called the mantle edge. The fissura longitudinalis cerebri is the cleft that divides the cerebrum in half. The cerebrum is called the telencephalon and the two halves of the brain are the right and left hemispheres. The edge of the mantle runs centrally above the brain from front to back.
It forms the transition from the outer to the inner surface of the brain. The hard meninges or dura mater encephali are located in the edge of the mantle. Its job is to give the brain mechanical support. Mantle edge syndrome is damage to the mantle edge of the cerebral hemisphere. This means that the function of the superior cerebral margin, the blunt edge at the transition from the convex part of the cortex to the medial surface on the hemisphere, is impaired.
The result is primarily movement and sensitivity disorders in both legs. This can lead to parapateses and paralysis of the extremities. In addition, there is a micturition disorder in the sick.These are problems with emptying your bladder.
causes
The most common cause of mantle edge syndrome is a parasagittal meningioma. This is associated with a spastic parapatesis of the legs and uncontrollable emptying of the bladder. Meningioma is a brain tumor that patients often develop in adulthood. It is diagnosed in most cases between the ages of 40 and 60.
Women are affected significantly more often than men. A meningioma is characterized by slow growth of the brain tumor and its repressive appearance. For this reason, the cause of complaints is often only found after several months or years. Mantle edge syndrome affects both hemispheres of the brain. This leads to a dysfunction of the cortical representation fields.
The compression of the meningioma on the cortex leads to a contralateral or bilateral leg parate. The squeezing of the brain and thus the tissue damage can also have other causes. In extremely rare cases, the lesion of both hemispheres can be caused by external influences. For example, grazing shots in the middle of the head belong to it.
Objects falling onto the head can also cause damage to the edge of the jacket. The use of force, such as a severe blow to the top of the head, can also cause lesions to the cortex and the edge of the mantle.
Symptoms, ailments & signs
The symptoms of mantle edge syndrome mainly include sensorimotor paralysis of the legs and a bladder disorder. The patient empties uncontrollably. In addition, the initial dorsiflexor weakness is documented. The foot lifting muscles in the swing phase are disturbed.
This enables the leg to swing freely. As with the parateses of the legs, one or both feet can be affected. Some patients experience Jackson seizures. These are focal epileptic seizures. Individual body regions or the extremities are affected. In extreme cases, an entire half of the body can be affected.
In the case of mantle edge syndrome, disorders of the rectum can also occur. Analogous to the bladder disorder, only voluntary control over the external sphincter is lost. Gross neurological deficits also occur in the coat edge syndrome. These can all be traced back to functional disorders in the affected brain regions.
Diagnosis & course of disease
The diagnosis of coat edge syndrome is considered to be very difficult. It is often overlooked in examinations or not recognized over a long period of time and not properly assessed. The disease usually lasts for several years. The slow growth of the brain tumor is one of the reasons.
In addition, the lesions are often underestimated due to external influences and are not adequately investigated. In the course of the disease, the mantle edge syndrome must be differentiated from the spinal paraplegic syndrome. The diagnosis is usually made using an imaging test such as magnetic resonance imaging (MRI). The structure and the functional activity of the cortex are determined and the damage to the mantle edge is visible.
Complications
The coat edge syndrome usually leads to various types of damage and restrictions, which mainly occur in the patient's brain. This damage continues to lead to disorders of sensitivity and paralysis. This paralysis then leads to movement restrictions and other restrictions in the patient's everyday life.
Epileptic seizures also occur, which in the worst case can lead to injury or death of the patient. The coat edge syndrome significantly limits and reduces the quality of life of the person affected. Complaints can also occur when emptying the bladder or when defecating and thus also lead to psychological complaints. However, mental complaints do not occur due to the coat edge syndrome.
Mantle edge syndrome is treated with a surgical intervention on the patient's brain. Since this is a very serious procedure, it can also lead to various complications. The tumor cannot be completely removed in every case. In some cases, those affected may then be dependent on diapers. The life expectancy of the patient is not influenced by the coat edge syndrome. The movement restrictions can also be treated with the help of various therapies.
When should you go to the doctor?
Motor disorders are signs of existing irregularities. A doctor's visit is necessary as soon as locomotion is impaired or symptoms of paralysis occur. A doctor is required in the event of pain, impaired perception or discomfort. Further examinations should be carried out to clarify the cause. If the muscles that lift the feet can no longer be moved as usual, it is advisable to consult a doctor. In these situations, the affected person experiences a swing of the leg and has no control over the extremities. To improve health, see a doctor so that treatment can be started immediately.
If, in addition to the complaints of the legs, there are also inconsistencies when going to the toilet, these are further symptoms that must be clarified by a doctor. If the sphincter muscle cannot be subjected to voluntary control or if there are problems emptying the bladder, a doctor should be consulted. If wetting or defecation occurs during the day or night, a doctor's visit is advisable. This also applies to children who are still in the growth phase. If you have a seizure disorder, convulsions or a feeling of illness, a doctor should be consulted. If there are impairments in the fulfillment of everyday duties or if the well-being decreases significantly, the person concerned should consult a doctor and seek help.
Treatment & Therapy
Treatment of mantle edge syndrome is individual, depending on the type of hemispheric damage. If a brain tumor is diagnosed, the patient undergoes surgery. Here the meningenoma is surgically removed. The edge of the mantle is supplied by the anterior cerebral artery. If this supply is damaged, an attempt is made to restore it.
In the case of bladder and fecal incontinence, medication is attempted to regulate it. Alternatively, wearing diapers is recommended. The dorsiflexor weakness is accompanied orthopedically. This reduces the risk of tripping or falling. Orthoses can, for example, provide individual support. These are functional electrical stimulators that stimulate the surface of the foot and the muscles. Alternatively, a neuroimplant can be used.
You can find your medication here
➔ Medicines for bladder and urinary tract healthOutlook & forecast
The prognosis for mania is poor in most patients. If left untreated, a threat to life often develops. Reckless behavior, an increased risk of accidents and a high degree of self-overestimation put those affected in unfavorable situations. Conflicts often arise that lead to legal and health threats to the patient. The actions carried out during a manic period lead to the person concerned becoming incapacitated. This means that in the worst case, compulsory treatment is necessary and can be initiated.
The symptoms improve significantly in therapeutic and medical care. In addition to the strong euphoric mood, there are also times of very depressive energy. Many patients are at risk of suicide and are therefore very likely to choose to end their lives prematurely. Long-term therapy is necessary to restore health stability. If it is accepted and the patient works with this therapy, the chances of an alleviation of the health irregularities increase.
Under optimal conditions, there are times when there are no symptoms and there is a significant improvement in the overall situation. An independent life can take place, so that the person concerned does not need any further daily care. Nevertheless, a regression of the existing complaints can be expected at any time in the course of life.
prevention
Basic preventive measures are not to be taken in the case of coat edge syndrome. If the cause is a brain tumor, there is no advance therapy for this rare disease or indications such as contaminated genetic material that could be taken into account. Since external influences can influence the lesions of the hemispheres, protective measures can be taken here.
Preventive protective measures should be taken in particular during activities or in places where there are falling objects. In these cases, the skullcap can be protected by wearing a helmet.
Aftercare
As with all tumorous diseases, the coat edge syndrome requires close follow-up after treatment. The aim of this is to build up a quality of life in spite of the illness and to guarantee it in the long term. In the case of a brain tumor, follow-up checks are therefore carried out several times a year at intervals of a few months.
If no abnormalities are found, the intervals between the next inspection will increase. Since the coat edge syndrome goes hand in hand with such severe cuts in everyday life, conditions suitable for everyday use should be developed in the course of aftercare that improve the handling of the situation.
Drug treatment will continue to be essential to relieve any pain that may arise. However, if unusual physical deficits become apparent outside of the follow-up controls, this should be reported to the attending physician as soon as possible. This will initiate an intensification of the follow-up treatment as soon as possible.
You can do that yourself
People suffering from coat edge syndrome have few options for self-help. If the disease is due to a brain tumor, surgery is necessary. During the treatment period, the guidelines of the doctors should be followed for the prospect of a good recovery.
Since the syndrome is a serious illness, the patient needs not only physical reserves but also sufficient mental strength to deal with the symptoms. A balanced diet rich in vitamins is valuable to support the immune system. The consumption of pollutants and toxins must be completely avoided.
In particular, the consumption of alcohol or nicotine should be avoided. Emotional stability can be promoted through various relaxation techniques. Qi Gong, autogenic training, yoga or meditation have often proven their worth. The patient can use these methods independently and independently.
Regular exchanges with people they trust or in self-help groups are beneficial for many of those affected. Experiences are discussed and tips for living with the disease are given. In spite of the limited possibilities, the patient should pursue leisure activities to strengthen his well-being. Everyday life has to be restructured so that it is optimally aligned with the needs of the patient. Studies have shown that positive thinking and an optimistic attitude are helpful in managing the condition.
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